probable major neurocognitive disorder due to frontotemporal lobar degeneration, without
behavioral disturbance.
For possible major neurocognitive disorder due to frontotemporal lobar degeneration, code
331.9 (G31.9)  possible major neurocognitive disorder due to frontotemporal lobar degen-
eration. ( Note:  Do not use the additional code for frontote mporal disease. Behavioral distur-
bance cannot be coded but should still be indicated in writing.)
For mild neurocognitive disorder due to frontotemporal lobar degeneration, code 331.83
(G31.84).  (Note:  Do not use the additional code for frontotemporal disease. Behavioral
disturbance cannot be coded but should still be indicated in writing.)
Diagnostic Features
Major or mild frontotemporal neurocognitive  disorder (NCD) comprises a number of syn-
dromic variants characterized by the progressi ve development of behavioral and personality
change and/or language impairment. The behavioral variant and three language variants (se-
mantic, agrammatic/nonfluent, and logopenic) ex hibit distinct patterns of brain atrophy and
some distinctive neuropathology. The criteria must be met for either the behavioral or the lan-
guage variant to make the diagnosis, but many  individuals present with features of both.
Individuals with behavioral-variant major or mild frontotemporal NCD present with
varying degrees of apathy or disinhibition. They may lose interest in socialization, self-
care, and personal responsibilities, or displa y socially inappropriate behaviors. Insight is
usually impaired, and this often delays medical consultation. The first referral is often to a
psychiatrist. Individuals may develop changes in  social style, and in religious and political