Major or Mild Frontotemporal Neurocognitive Disorder 615
2. Language variant:
a. Prominent decline in language ability, in the form of speech production, word
finding, object naming, grammar, or word comprehension.
D. Relative sparing of learning and memory and perceptual-motor function.
E. The disturbance is not better explained by cerebrovascular disease, another neurode-
generative disease, the effects of a substance, or another mental, neurological, or sys-
temic disorder.
Probable frontotemporal neurocognitive disorder  is diagnosed if either of the following
is present; otherwise, possible frontotemporal neurocognitive disorder  should be di-
agnosed: 
1. Evidence of a causative frontotemporal neur ocognitive disorder genetic mutation, from
either family history or genetic testing.
2. Evidence of disproportionate frontal and/or temporal lobe involvement from neuroim-
aging.
Possible frontotemporal neurocognitive disorder  is diagnosed if there is no evidence
of a genetic mutation, and neuroimaging has not been performed.
Coding note: For probable major neurocognitive disorder due to frontotemporal lobar de-
generation, with behavioral disturbance, code first 331.19 (G31.09) frontotemporal dis-
ease, followed by 294.11 (F02.81)  probable major neurocognitive disorder due to
frontotemporal lobar degeneration, with behavioral disturbance. For probable major neu-
rocognitive disorder due to frontotemporal  lobar degeneration, without behavioral distur-
bance, code first 331.19 (G31.09) frontotemporal disease, followed by 294.10 (F02.80)
probable major neurocognitive disorder due to frontotemporal lobar degeneration, without