(Do not use addi-
tional code for 
Alzheimer’s 
disease.)
Frontotemporal 
lobar degeneration Probable: 331.19 
(G31.09)
Possible: no additional 
medical codeProbable: 294.1x 
(F02.8x)
Possible: 331.9 
(G31.9)c331.83 (G31.84) 
(Do not use addi-
tional code for 
frontotemporal 
disease.)
Lewy body disease Probable: 331.82 
(G31.83)
Possible: no additional 
medical codeProbable: 294.1x 
(F02.8x)
Possible: 331.9 
(G31.9)c331.83 (G31.84) 
(Do not use addi-
tional code for 
Lewy body disease.)
Vascular disease No additional medical 
codeProbable: 290.40 
(F01.5x)
Possible: 331.9 
(G31.9)c331.83 (G31.84) 
(Do not use addi-
tional code for the 
vascular disease.)
Traumatic brain 
injury907.0 (S06.2X9S) 294.1x (F02.8x) 331.83 (G31.84)
(Do not use additional 
code for the trau-
matic brain injury.)
Substance/
medication-
inducedNo additional medical 
codeCode based on the 
type of substance 
causing the major 
neurocognitive 
disorderc, dCode based on the 
type of substance