Present in SCA8-specific 1C2-positive intranuclear inclusions. Specifically found in brains from SCA8 patients (at protein level). The length of the poly-Gln expansion is variable and may contain one or more interruptions that introduce arginines into the polyglutamine repeat tract. The disease is caused by variants affecting the gene represented in this entry. It is unknown whether this protein exists in non-SCA8 individuals.