May play a role in actin filament architecture in developing stereocilia of sensory cells. In the inner ear, localized to stereocilia, apical microvilli of sensory cells and kinocilia. Expressed at low levels in adult lung, brain and duodenum with moderate levels in testis. Highly expressed in fetal cochlea. The disease is caused by variants affecting the gene represented in this entry. Belongs to the GRXCR1 family.