Mitochondrial protein implicated in negative regulation of leucine tRNA levels, as well as negative regulation of mitochondria-encoded proteins and COX activity. Affects also the 3'-processing of mitochondrial tRNAs. Associates with mitochondrial leucine tRNAs. Interacts with ELAC2. Abundant in testes, skeletal muscle and heart. Belongs to the PTCD1 family. Extended N-terminus.