Transcriptional repressor. Specifically binds DNA and probably acts by recruiting chromatin remodeling multiprotein complexes. In skeletal myofibers, highly enriched in subsynaptic nuclei at the neuromuscular junctions. Expressed in skeletal muscle (at protein level). The disease is caused by variants affecting the gene represented in this entry. Belongs to the krueppel C2H2-type zinc-finger protein family. ZBTB18 subfamily.