Component of the centrioles controlling mother and daughter centrioles length. Involved in the biogenesis of the cilium, a centriole-associated function. The cilium is a cell surface projection found in many vertebrate cells required to transduce signals important for development and tissue homeostasis. Plays an important role in development by regulating Wnt signaling and the specification of the left-right axis. Localizes to centriole distal ends. Widely expressed. Embryos display several alterations during development including perturbed intravesicular fluid flow in Kuppfer's vesicle, convergent extension defects and randomization of laterality of organs. Belongs to the OFD1 family.