Required for osteoclast and melanocyte maturation and function. Chloride channel 7 are heteromers of alpha (CLCN7) and beta (OSTM1) subunits. Requires CLCN7 to travel to lysosomes. Undergoes proteolytic cleavage in the luminal domain, the cleaved fragments might be linked by disulfide bonds with the remnant of the protein. Highly N-glycosylated. The disease is caused by variants affecting the gene represented in this entry. Belongs to the OSTM1 family.