Involved in primary cilium formation (PubMed:19852954, PubMed:28530676). Probably acts as a transition zone protein required for localization of PKD1/PC1 and PKD2/PC2 to the ciliary membrane (PubMed:28530676). Interacts with SEPTIN2 (PubMed:28530676). Localizes to centrioles and to the distal ends of basal bodies (PubMed:28530676). The disease is caused by variants affecting the gene represented in this entry. Belongs to the DZIP C2H2-type zinc-finger protein family.