May play a role in modulation of fibrillin microfibrils in the extracellular matrix (ECM). Interacts with heparin, FBN1 and FBN2. Colocalized with fibrillin microfibrils. Predominantly distributed in baso-lateral regions of fibroblast extracellular matrix. Proteolytically cleaved to release a C-terminal fragment containing the NTR domain. Contains at least one additional N-linked glycosylation site. Major. Minor. Although strongly similar to members of the ADAMTS family it lacks the metalloprotease and disintegrin-like domains which are typical of that family.