Nucleolar protein that is involved in ribosomal RNA (rRNA) processing (PubMed:33199730). Also plays a role in primary cilia resorption, and cell cycle progression in neurogenesis and neocortex development (PubMed:33199730). Interacts with NOL6; required for NOL6 localization to nucleolus. Expressed in the apical radial glial cells in the developing brain. The disease is caused by variants affecting the gene represented in this entry. Belongs to the RRP7 family. Truncated N-terminus.