<unk>  is a very rare heart defect (affecting 3 per million live births) in which the aorta is not completely developed. There is a gap between the ascending and descending thoracic aorta. In a sense it is the complete form of a coarctation of the aorta. Almost all patients also have other cardiac anomalies, including a ventricular septal defect (VSD), aorto-pulmonary window, and truncus arteriosus. There are three types of<unk> , with type B being the most common.<unk>  (especially Type B) is often associated with DiGeorge syndrome.
Interrupted aortic arch
Double aortic arch
First arch syndrome
Right-sided aortic arch
Situs ambiguus
Persistent truncus arteriosus
Crisscross heart
Tricuspid atresia