To reduce the levels of<unk>  in the blood, a diet restricted in arginine has been used. Some research has shown that when diet or other treatment is initiated early in life, the outcome can be improved.
Ornithine aminotransferase deficiency
Glutaminase deficiency
Malonyl-CoA decarboxylase deficiency
Pyruvate kinase deficiency
Arginine:glycine amidinotransferase deficiency
3-Hydroxyisobutyryl-CoA deacylase deficiency
3-Methylcrotonyl-CoA carboxylase deficiency
Transaldolase deficiency