<unk>  is an inherited disorder that causes ammonia to accumulate in the blood. Ammonia, which is formed when proteins are broken down in the body, is toxic if the levels become too high. The nervous system is especially sensitive to the effects of excess ammonia.
Carbamoyl phosphate synthetase I deficiency
Pyruvate kinase deficiency
Alpha-ketoglutarate dehydrogenase deficiency
Ornithine translocase deficiency
Triosephosphate isomerase deficiency
ALA dehydratase deficiency
Fructose bisphosphatase deficiency
Carnitine palmitoyltransferase II deficiency