<unk>  is a disorder resulting from proliferation of abnormal smooth muscle like cells, mostly in the lungs but can also occur in other body parts such as kidney, mediastinum or axial lymphatics.<unk>  is characterized by small mediastinal or retro- peritoneal tumors which involve the thoracic duct and consist of numerous smooth muscle bundles interspersed with lymphatic channels.<unk>  must be differentiated from other diseases that cause similar clinical features, such as asthma, spontaneous pneumothorax, emphysema, interstitial pulmonary fibrosis, eosinophilic granuloma (EG), Birt-Hogg-Dube syndrome, lymphangiomas, pulmonary lymphangiectasis, and leiomyosarcoma. Symptoms of<unk>   may include constipation, dyspnea, and cough. The mainstay of therapy for<unk> is include sirolimus, medroxyprogesterone, gonadotropin-releasing hormone agonists, and tamoxifen. The most effective treatment is lung transplant.
Lymphangiomyomatosis
Lymphangitis carcinomatosa
Fibromatosis
Bacillary angiomatosis
Angiomatosis
Angiosarcoma
Arteriosclerosis obliterans
Mycotic aneurysm