<unk>  is a benign renal neoplasm previously considered to be a hamartoma or choristoma, but now known to be neoplastic. It is composed of variable amounts of fat, vascular, and smooth muscle elements. The fat density of the tumor on CT scan has been regarded to be pathognomonic. The lesion is well demarcated and contains mature elements. It occurs in more than 50% of individuals with tuberous sclerosis, often bilaterally. On gross pathology, well circumscribed and uniform yellow mass is characteristic finding of<unk> .<unk>  is caused by a defect in the TSC1 gene.<unk>  must be differentiated from retroperitoneal liposarcoma, adrenal myelolipoma, and renal cell carcinoma. If left untreated, small<unk> s and those without dilated blood vessels (aneurysms) cause few symptoms. Small<unk> s are associated with the most favorable prognosis. Common complications of<unk>  include infection, hematuria and hemorrhage. Abdominal CT scan may be diagnostic for<unk> . On CT scan,<unk>  is characterized by smooth tumor margin with low intratumoral fat component and homogenous enhancement on both corticomedullary and excretory phase scans. Surgery is not the first-line treatment option for patients with<unk> . Transcatheter arterial embolization is usually reserved for patients with complicated disease.
Angiomyolipoma
Adrenolipoma
Fibroadenolipoma
Adrenal myelolipoma
Renal oncocytoma
Oncocytoma
Metanephric adenoma
PEComa