Congenital hepatic fibrosis Congenital hepatic fibrosis Congenital hepatic fibrosis is an inherited fibrocystic liver disease associated with proliferation of interlobular bile ducts within the portal areas and fibrosis that do not alter hepatic lobular architecture. The fibrosis would affect resistance in portal veins leading to portal hypertension. The condition is usually congenital, but sporadic cases have also been reported. It may be associated with other congenital defects, commonly with autosomal recessive polycystic kidney disease, the most severe form of PKD. Some suggest that these two conditions are one disorder with different presentation. Embryogenically, congenital hepatic fibrosis is due to malformation of the duct
Convention for the Protection of Human Rights and Dignity of the Human Being with regard to the Application of Biology and Medicine availability of organs from a deceased person. Any removed parts of the body must be disposed of respectfully in accordance with the wishes of the individual. In addition, there is to be no financial gain arising from the human body or its parts, however adequate compensation for expenses incurred for a medical procedure is not prohibited. The rules relating to consent laid out in "Chapter II" of the Convention also apply in the context of organ transplantation. In accordance with the European Convention on Human Rights, any individual who has suffered damage should have access to fair compensation ("Article 24").