Mount Elbrus Russia. The name "Elbrus" is a metathesis of "Alborz", which is also the name of a long mountain range in northern Iran. It is derived from Avestan "Harā Bərəzaitī", which is a legendary mountain in Iranian mythology. "Harā Bərəzaitī" reflects Proto-Iranian *"Harā Bṛzatī", which was reformed into Middle Persian as "Harborz", and into Modern Persian as "Alborz". "Bṛzatī" is the feminine form of the adjective *"bṛzant" ("high"), the reconstructed ancestor of Modern Ossetian "bærzond" ("high", "peak"), Modern Persian "barz" ("high"), "berāzande" ("elegant"), and "boland" ("high", "tall"), and Modern Kurdish "barz" ("high"). "Harā" may be interpreted as "watch" or "guard", from
MT-ND3 mtDNA-associated Leigh syndrome, as are variants of MT-ATP6, MT-TL1, MT-TK, MT-TW, MT-TV, MT-ND1, MT-ND2, MT-ND4, MT-ND5, MT-ND6 and MT-CO3. Abnormalities in mitochondrial energy generation result in neurodegenerative disorders like Leigh syndrome, which is characterized by an onset of symptoms between 12 months and three years of age. The symptoms frequently present themselves following a viral infection and include movement disorders and peripheral neuropathy, as well as hypotonia, spasticity and cerebellar ataxia. Roughly half of affected patients die of respiratory or cardiac failure by the age of three. Leigh syndrome is a maternally inherited disorder and its diagnosis is established through