A glycogen storage disease (GSD) results from the absence of enzymes that ultimately convert glycogen compounds to glucose. Enzyme deficiency results in glycogen accumulation in tissues.In many cases, the defect has systemic consequences, but, in some cases, the defect is limited to specific tissues.onversion generally is a one-way reaction from glycogen to glucose-1,6-phosphate. The enzyme is found in all tissues. Disease results from a pan-deficiency of the enzyme (GSD IIIa) or muscle-specific retention of glycogen debranching enzyme (GSD IIIb). The condition is autosomal recessive.
COMPANY OVERVIEW. GREENBRIER INTERNATIONAL INC is in the Variety Stores industry in CHESAPEAKE, VA. This company currently has approximately 10,000 to 25,000 employees and annual sales of $500,000,000 to $999,999,999.
The Greenbrier is a palatial luxury resort located in the Allegheny Mountains near White Sulphur Springs in Greenbrier County, West Virginia, in the United States. Since 1778, visitors have traveled to this part of the state to take the waters of the area. Today, The Greenbrier is situated on 11,000 acres of land with 710 guest rooms, 20 restaurants and lounges, more than 55 indoor and outdoor activities and sports, and 36 retail shops. 1800 ladies and gentlemen offer authentic southern hosp