Best Answer: Sucrose (common name: table sugar, also called saccharose) is a disaccharide (glucose + fructose) with the molecular formula C12H22O11. Its systematic name is Î±-D-glucopyranosyl-(1â2)-Î²-D-fructofuran...
The classic form of infantile-onset Pompe disease begins within a few months of birth. Infants with this disorder typically experience muscle weakness (myopathy), poor muscle tone (hypotonia), an enlarged liver (hepatomegaly), and heart defects.
Symptoms & Signs. As mentioned earlier, the pompe disease can affect infants, children and adults alike. The infants who have this disease will manifest the following symptoms: weakness of the muscles. enlargement of the liver and heart. breathing problems. unable to eat well. dysphagia or swallowing difficulties. enlarge tongue.