Best Answer: Sucrose (common name: table sugar, also called saccharose) is a disaccharide (glucose + fructose) with the molecular formula C12H22O11. Its systematic name is Î±-D-glucopyranosyl-(1â2)-Î²-D-fructofuran...
The classic form of infantile-onset Pompe disease begins within a few months of birth. Infants with this disorder typically experience muscle weakness (myopathy), poor muscle tone (hypotonia), an enlarged liver (hepatomegaly), and heart defects.
The main signs and symptoms are shown in Table 1. Not all people with the condition have all these signs and symptoms. Some people have few or âmildâ symptoms â perhaps just weight gain and irregular menstrual periods. Other people with a more âsevereâ form of the disease may have nearly all the symptoms. The most common symptoms in adults are weight gain (especially in the trunk, and often not accompanied by weight gain in the arms and legs), high blood pressure (hypertension), and changes in memory, mood and concentration.