Best Answer: Sucrose (common name: table sugar, also called saccharose) is a disaccharide (glucose + fructose) with the molecular formula C12H22O11. Its systematic name is Î±-D-glucopyranosyl-(1â2)-Î²-D-fructofuran...
The classic form of infantile-onset Pompe disease begins within a few months of birth. Infants with this disorder typically experience muscle weakness (myopathy), poor muscle tone (hypotonia), an enlarged liver (hepatomegaly), and heart defects.
The Symptoms of LEMS. The onset of LEMS is gradual and symptoms start with slowly progressive muscle weakness and fatigue; muscle aches and cramps are also frequent. The weakness commonly involves muscles of the hips and legs on both sides at the same time and can sometimes cause significant impairment of activities of daily living.