A twist on popular polished granite, honed granite gives a soft, matte finish instead of the traditional glossy look. Like polished granite, honed granite is just as resistant to scratching, chipping, cracking and heat, making it one of the most durable kitchen countertop options around.
Galactosemia (Galactosaemia) is a rare genetic metabolic disorder that affects an individual's ability to metabolize the sugar galactose properly. Galactosemia is not related to and should not be confused with lactose intolerance. Galactosemia follows an autosomal recessive mode of inheritance that confers a deficiency in an enzyme responsible for adequate galactose degradation. Goppert first described the disease in 1917, with its cause as a defect in galactose metabolism being identified by a group led by Herman Kalckar in 1956.
Fig. 1 â beta-D-Galactopyranose. Galactose, sometimes abbreviated Gal, is a monosaccharide and the C4 epimer of glucose, that is, they differ only for the position of the-OH group on C4 (axial in Gal, equatorial in glucose).It has a sweetness equal to 33% of sucrose.n hepatocytes, galactose enters the Leloir pathway. Freed from lactose, the monosaccharide is mostly present as beta-isomer, and the first step of its hepatic metabolism is the conversion to the alpha-isomer, in the reaction catalyzed by galactose mutarotase (also known as aldose 1-epimerase).