Definition of White blood cell count. White blood cell count (leukocyte count): The number of white blood cells (WBCs) in the blood. The WBC is usually measured as part of the CBC (complete blood count). White blood cells are the infection-fighting cells in the blood and are distinct from the red (oxygen-carrying) blood cells known as erythrocytes.
The disease is named for the presence of sweet-smelling urine, with an odor similar to that of maple syrup, when the person goes into metabolic crisis. The smell is also present and sometimes stronger in the ear wax of an affected individual at these times.
Maple syrup urine disease (MSUD) is a rare, inherited metabolic disorder. With MSUD, the body cannot break down certain amino acids. Individuals who have the disease produce urine that has a distinctive maple syrup odor. Amino acids are what remain after your body digests the protein from the food you eat. Special enzymes process the amino acids so they can be used to maintain all of your body functions.