aragonite; aragonitic; AraguaÃ­a; Araguaia River; Araguato; Araguaya; Araguaya River; arain; araise; arak; Arakan Yoma; Araks; Aral Sea; Araldite; Arales; aralia; Aralia elata; Aralia hispida; Aralia nudicaulis; Aralia racemosa; Aralia spinosa; Aralia stipulata; Araliaceae; araliaceous; Aram; Aram Ilich Khachaturian; Aram Kachaturian
Krabbe disease (also known as globoid cell leukodystrophy or galactosylceramide lipidosis) is a rare, often fatal degenerative disorder that affects the myelin sheath of the nervous system.It is a form of sphingolipidosis, as it involves dysfunctional metabolism of sphingolipids.he disease is named after the Danish neurologist Knud Haraldsen Krabbe (1885-1965). Illinois, Kentucky and Pennsylvania have laws to test for Krabbe and other diseases at birth. There is a movement in Maine and other states to adopt such regulations.
Krabbe disease is very rare. According to the Mayo Clinic, the disease affects about one in every 100,000 people in the United States (Mayo Clinis, 2011). It occurs most frequently in people of Scandinavian descent. A child has a one in four chance of developing the disorder if both parents have the defective gene.