Peter is a mischievous 12-year-old boy with an irrepressible rebellious streak, but in the bleak London orphanage where he has lived his whole life those qualities do not exactly fly....
Chiari malformation, also known as an Arnold-Chiari malformation, is a congenital (present at birth) defect occurring in the back of the head where the brain and spinal cord connect.There are four types of Chiari malformations:1  Type 1 â Occurring when the base of the skull and upper spinal area do not form properly, a type 1 Chiari malformation commonly goes unnoticed until problems arise in the adolescent or adult years of life.here are four types of Chiari malformations: 1  Type 1 â Occurring when the base of the skull and upper spinal area do not form properly, a type 1 Chiari malformation commonly goes unnoticed until problems arise in the adolescent or adult years of life.
Headache was also common (about 80%). These symptoms overlap with those of Meniereâs disease as well as to lesser extent, migraine (Sperling et al, 2001) Signs of a significant Chiari malformation often include downbeat nystagmus, poor visual pursuit for age, and alternating skew deviation. Occasionally patients will have sensorineural hearing loss Heuer et al., 2008). A few individuals with the Chiari malformation develop progressive neurological symptoms. These may include unsteadiness, vertigo, headache, weakness or numbness.