Soil water status as a function of pressure (tension). Soil water status in natural soils can range from a flooded. condition to drainable gravitational water to plant available water. down to hydroscopic water. Tensions in natural soils do not. exceed -31,000; in this range, water is absorbed from the air.
Advanced Search. Tay-Sachs disease (the most severe form of Hexosaminidase A deficiency) is a progressive, fatal genetic condition that affects the nerve cells in the brain.
Tay-Sachs and Sandhoff diseases are rare, inherited diseases that affect a babyâs central nervous system (the brain and spinal cord). The central nervous system controls how the body works. Sandhoff disease is a severe form of Tay-Sachs. Babies with Tay-Sachs have none or not enough of an enzyme (protein) called hexosaminidase A.