Soil water status as a function of pressure (tension). Soil water status in natural soils can range from a flooded. condition to drainable gravitational water to plant available water. down to hydroscopic water. Tensions in natural soils do not. exceed -31,000; in this range, water is absorbed from the air.
Advanced Search. Tay-Sachs disease (the most severe form of Hexosaminidase A deficiency) is a progressive, fatal genetic condition that affects the nerve cells in the brain.
Tay-Sachs disease is an inherited disease caused by an abnormal gene. People with this abnormal gene do not have an important enzyme called hexosaminidase A (HEXA) that helps to break down a fatty material called ganglioside GM2. This material builds up in the brain, and eventually damages nerve cells and causes neurological problems.