The adrenal medullaâthe inner part of the glandâproduces nonessential (that is, you donât need them to live) hormones, such as adrenaline (which helps your body react to stress). When you think of the adrenal glands (also known as suprarenal glands), stress might come to mind.
Pyruvate dehydrogenase complex deficiency (PDCD) is a rare disorder of carbohydrate metabolism caused by a deficiency of one of the three enzymes in the pyruvate dehydrogenase complex (PDC). The age of onset and severity of disease depends on the activity level of the PDC enzymes.
Traditionally the inherited metabolic diseases were classified as disorders of carbohydrate metabolism, amino acid metabolism, organic acid metabolism, or lysosomal storage diseases. In recent decades, hundreds of new inherited disorders of metabolism have been discovered and the categories have proliferated.