When she doesn't have a thing to do. She comes to my house. Well, let's keep that between me and you. She takes off her clothes. She likes to tell this boy what to do. Let's keep that between me and you, ok. She said oh come on boy aren't you tired of talking about sex. I said little girl what do you really expect.
Maple syrup urine disease caused by mutation in the E1-alpha subunit gene is referred to as MSUD type IA; that caused by a mutation in the E1-beta subunit gene as type IB; and that caused by defect in the E2 subunit gene as type II. number sign (#) is used with this entry because maple syrup urine disease (MSUD) can be caused by homozygous or compound heterozygous mutation in at least 3 genes: BCKDHA (608348) on chromosome 19q13, BCKDHB (248611) on chromosome 6q14, and DBT (248610) on chromosome 1p21.
Maple syrup urine disease (MSUD) was one of the earliest and best known of the inborn errors of amino acid metabolism primarily because it was associated with an odor in the urine strongly reminiscent of maple syrup.