Examples of carboxylic acids The name counts the total number of carbon atoms in the longest chain-including the one in the-COOH group. If you have side groups attached to the chain, notice that you always count from the carbon atom in the-COOH group as being number 1.
The most common inherited diseases are von Willebrand disease (primary hemostasis), which is the most common inherited disorder of hemostasis, and hemophilia A (factor VIII deficiency, secondary hemostasis). Inherited disorders of the blood vessel wall, platelet number, platelet function, and inhibitors are quite rare.
Practice Essentials. Wilson disease is a rare autosomal recessive inherited disorder of copper metabolism that is characterized by excessive deposition of copper in the liver, brain, and other tissues (see the image below). Wilson disease is often fatal if not recognized and treated when symptomatic.