The prevalence of an early repolarization pattern on ECG with J point elevation in the inferior or lateral leads of at least 0.1 mV has been reported to be as high as 5.8% in adultsS7.9.1.4-1 and is more common in males. The early repolarization pat- tern was lost during 10-year follow-up in >60% of young males.S7.9.1.4-2 Patients are determined to have an early repolarization syndrome when, in addition to having early repolarization pattern on an ECG, they either have symptoms such as syncope or present with an arrhythmia. When patients present with an early repolarization pat- tern on an ECG, it is important to rule out revers- ible causes such as ischemia. Patients with early repolarization are more susceptible to the devel- opment of VF during acute cardiac ischemia and/ or in the presence of QRS abnormalities due to LV hypertrophy or bundle-branch block.S7.9.1.4-6 S7.9.1.4-8 2. Patients with cardiac arrest or VF in the setting of an electrocardiographic pattern of early repolar- ization are at increased risk for subsequent recur- rent episodes of VF, occurring in at least 40% Antiarrhythmic medications, with the exception of quindine/ hydroquinidine, have limited efficacy in prevent- ing recurrent VA.S7.9.1.4-3,S7.9.1.4-4 3. To date, genetic testing has not reliably identified mutations predisposing to early repolarization.S7.9.1.4-5 7.9.1.5. Short QT Syndrome Recommendations for Short QT Syndrome References that support the recommendations are summarized in Online Data Supplement 44. 