Pulmonary hypertension is defined as: Mean PA pressure by right heart catheterization 25 mmHg. PAH is defined as: Mean PA pressure by right heart catheterization 25 mmHg and a pulmonary capillary wedge pressure 15 mmHg and pulmonary vascular resistance 3 Wood unitsS2.2-20 Shunt (hemodynamically significant shunt) An intracardiac shunt is hemodynamically significant if: There is evidence of chamber enlargement distal to the shunt And/or evidence of sustained Qp:Qs 1.5:1 An intracardiac shunt not meeting these criteria would be described as small or trivial Venous and arterial stenosis Aortic recoarctation after CoA repair Supravalvular aortic obstruction Venous baffle obstruction Supravalvular pulmonary stenosis Branch PA stenosis Stenosis of cavopulmonary connection Pulmonary vein stenosis ACHD indicates adult congenital heart disease; AF, atrial fibrillation; AP, anatomic and physiological; CHD, congenital heart disease; CoA, coarctation of the aorta; CPET, cardiopulmonary exercise test; HF, heart failure; ICD, implantable cardioverter-defibrillator; NYHA, New York Heart Association; PA, pulmonary artery; PAH, pulmonary arterial hypertension; Qp:Qs, pulmonary systemic blood flow ratio; and VHD, valvular heart disease. Table 3. Continued Variable Description CLINICAL STATEMENTS AND GUIDELINES Table 4. 