An initial exten- sive evidence review, which included literature de- rived from research involving human subjects, pub- lished in English, and indexed in MEDLINE (through PubMed), EMBASE, the Cochrane Library, the Agency for Healthcare Research and Quality, and other select- ed databases relevant to this guideline, was conduct- ed from April 2014 to November 2014. Key search words included but were not limited to the follow- ing: adult congenital heart disease, anesthesia, aortic aneurysm, aortic stenosis, atrial septal defect, arterial switch operation, bradycardia, bicuspid aortic valve, cardiac catheterization, cardiac imaging, cardiovas- cular magnetic resonance, cardiac reoperation, car- diovascular surgery, chest x-ray, cirrhosis, coarctation of the aorta, congenital heart defects, congenitally corrected transposition of the great arteries, con- traception, coronary artery abnormalities, cyanotic congenital heart disease, dextro-transposition of the great arteries, double inlet left ventricle, Ebstein a- nomaly, echocardiography, Eisenmenger syndrome, electrocardiogram, endocarditis, exercise test, Fon- tan, heart catheterization, heart defect, heart failure, infertility, l-transposition of the great arteries, medical therapy, myocardial infarction, noncardiac surgery, patent ductus arteriosus, perioperative care, physical activity, postoperative complications, pregnancy, pre- operative assessment, psychosocial, pulmonary arte- rial hypertension, hypoplastic left heart syndrome, pulmonary regurgitation, pulmonary stenosis, pul- monary valve replacement, right heart obstruction, right ventricle to pulmonary artery conduit, single ventricle, supravalvular pulmonary stenosis, surgical therapy, tachyarrhythmia, tachycardia, tetralogy of Fallot, transplantation, tricuspid atresia, Turner syn- drome, and ventricular septal defect. Additional rele- vant studies published through January 2018, during the guideline writing process, were also considered by the writing committee, and added to the evidence tables when appropriate. The final evidence tables, included in the Online Data Supplement, summarize the evidence used by the writing committee to for- mulate recommendations. References selected and published in this document are representative and not all-inclusive. 