Idiopathic Pulmonary Fibrosis By Joyce Lee, MD, MAS, University of Colorado School of Medicine Reviewed / Revised Jun 2021 | Modified Sep 2022 View Patient Education Etiology Pathology Symptoms and Signs Diagnosis Prognosis Treatment Key Points Topic Resources Idiopathic Pulmonary Fibrosis Idiopathic pulmonary fibrosis (IPF), the most common form of idiopathic interstitial pneumonia, causes progressive pulmonary fibrosis.