turricephaly turricephaly turricephaly is a type of cephalic disorder where the head appears tall with a small length and width. it is due to premature closure of the coronal suture plus any other suture, like the lambdoid, or it may be used to describe the premature fusion of all sutures. it should be differentiated from crouzon syndrome. oxycephaly (or acrocephaly) is a form of turricephaly where the head is cone-shaped, and is the most severe of the craniosynostoses. turricephalyother namesoxycephaly, acrocephaly, hypsicephaly, oxycephalia, steeple head, tower head, tower skull, high-head syndrome, turmschädelspecialtydysmorphologysymptomsreduced head length and width for age presentation common associations it may be associated with: 8th cranial nerve lesion optic nerve compression intellectual disability syndactyly conditions with turricephaly achondrogenesis type 1a acrocephalopolydactyly acrocephalosyndactyly type v (goodman syndrome) acrocraniofacial dysostosis megf8-related carpenter syndrome pfeiffer syndrome potocki-shaffer syndrome saethre-chotzen syndrome spondyloenchondrodysplasia with immune disregulation spondyloepimetaphyseal dysplasia, sedaghatian type summitt syndrome twist1-related craniosynostosis congenital syphilis hydrocephalus microcephaly pfeiffer syndrome saethre-chotzen syndrome diagnosis