The author study the clinical histories and the histopathologic findings in five patients who were hospitalized in the National Oncological Institute, between 1983 and 1993 in whom the diagnosis of Dermatofibrosarcoma protuberans was established. He note the age, sex, localization of the tumor, the frequency and cause of recurrence; he discuss the differential diagnosis with benign fibrous histiocytoma and neurofibroma and, since recurrence may exhibit mixoid changes (as occurred in two of the cases), also discuss the differential diagnosis with mixoid liposarcoma and mixoid malignant fibrous histiocytoma and pseudo sarcomatous nodular fascitis.
Adolescent Adult