tokens: In patients with type IA maple syrup urine disease , the E1alpha subunit is affected , resulting in the loss of E1 and branched-chain ketoacid dehydrogenase catalytic activities .
folded_tokens: in patient with type ia maple syrup urine disease , the e1alpha subunit be affect , result in the loss of e1 and branched-chain ketoacid dehydrogenase catalytic activity .