Introduction:Skin tumors are prevalent in the head and neck especially auricle but pilomatricoma is extremely rare in ear lobule.Case Report:A 7-year-old girl without a history of previous illness presented with a 1.5-month historyof a lesion in theright ear lobulethat tended to grow in size. It was a 2*2*2cmround, slightly painful lesionwithsofttissue and light red in color that yielded bloody orserous fluid on aspiration. The lesion was enucleated. The diagnosis was pilomatricoma.Conclusion:Although very rare, pilomatricoma should be considered as a differential diagnosis of ear lobule neoplasms.