AbstractInternal jugular venous aneurysm (IJVA) is a rare cause of neck swelling that usually remains asymptomatic unless there are complications. We report a case of an aneurysm in a duplicated IJV. Our patient was diagnosed with a palpable soft tissue mass in the neck and was found to have IJVA on imaging. In this case, the duplicated IJV aneurysm was resected, leaving a single internal jugular vein as the main vein draining the ipsilateral head and neck with excellent outcome. The most common indication for surgery is usually cosmetic.