Many patients present to our clinic withHelicobacter pylori(H. pylori) infection. Most have nonspecific symptoms that cannot be immediately attributed toH. pylori. The joint European Society for Paediatric Gastroenterology, Hepatology, and Nutrition (ESPGHAN)/North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition (NASPGHAN) guidelines recommend upper gastroscopy to detect the cause of such symptoms. Herein, we present the case of a 9-year-old girl diagnosed with gastric mucosa-associated lymphoid tissue lymphoma associated withH. pyloriinfection using upper gastroscopy. We believe that a patient of such a young age with this serious condition secondary toH. pyloriwill highlight the importance of upper gastrointestinal endoscopy in such cases.