What is Rhabdoid Tumor?

Rhabdoid tumor is a rare childhood tumor that commonly starts in the kidneys but can also occur in other soft tissues or in the brain.

What causes Rhabdoid tumor? Who is affected?

The causes are unknown, but genetic factors play an important role. Researchers have discovered that a gene called SMARCB1 is mutated in nearly all rhabdoid tumors, including malignant rhabdoid tumor and atypical teratoid rhabdoid tumor (ATRT). Mutations in this gene can also sometimes occur in a patient’s normal, non-tumor cells, increasing their risk of developing additional rhabdoid tumors. Children are mainly affected. The average age when children are diagnosed is 15 months old.

What are the symptoms for Rhabdoid tumor?

Symptoms for Rhabdoid tumor include:

  • Stomach pain
  • Cerebral palsy
  • Cranial nerve paralysis
  • Fever
  • Headache


How is Rhabdoid tumor treated?

There are many different treatments for rhabdoid tumor depending on stage and preference, including:

  • Surgery
  • Stem cell therapy
  • Chemotherapy
  • Radiation therapy

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