Macular dystrophy, vitelliform, adult-onset - Conditions - GTR - NCBI - adult onset vitelliform


adult onset vitelliform

Mar 08, 2016 · Adult-onset vitelliform macular dystrophy (AVMD) is an eye disorder that can cause progressive vision loss. AVMD affects an area of the retina called the macula, which is responsible for sharp central vision. The condition causes a fatty yellow pigment to accumulate in cells underlying the macula, eventually damaging the cells.

Adult-onset foveomacular vitelliform dystrophy, also known as adult vitelliform macular dystrophy, adult-type foveomacular dystrophy, adult vitelliform macular degeneration, pseudovitelliform macular degeneration, and adult-onset foveomacular pigment epithelial dystrophy, is characterized by a solitary, oval, slightly elevated yellowish subretinal lesion of the fovea that is similar in appearance to .

Vision loss is mild as in vitelliform 1 disease and only slowly progressive in most patients.   One or sometimes more small, oval, and slightly elevated yellow lesions resembling an egg yolk may be seen in the fovea along with paracentral drusen and mild RPE changes.

Vitelliform Macular Dystrophy -- adult-onset: Vitelliform macular dystrophy is a rare inherited eye disorder that affects the retina and often results in progressive loss of central vision. The adult-onset form of the condition usually appears during middle age and symptoms are generally not as severe as the early-onset form.