* MT-CYB: mtDNA encoded cytochrome b; mutations associated with exercise intolerance
* CYC1: cytochrome c1
* CYCS: cytochrome c
* UQCRFS1: Rieske iron sulfur protein
* UQCRB: Ubiquinone binding protein, mutation linked with mitochondrial complex III deficiency nuclear type 3
* UQCRH: hinge protein
* UQCRC2: Core 2, mutations linked to mitochondrial complex III deficiency, nuclear type 5
* UQCRC1: Core 1
* UQCR: 6.4KD subunit
* UQCR10: 7.2KD subunit
* TTC19: Newly identified subunit, mutations linked to complex III deficiency nuclear type 2. Helps remove the N-terminal fragment of UQCRFS1, which would otherwise interfere with complex III function.